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"CYSTIC FIBROSIS"

“ This is an autosomal recessive defect in the gene regulating chloride transport, resulting in thick secretions. The lungs and pancreas are...

This is an autosomal recessive defect in the gene regulating chloride transport, resulting in thick secretions. The lungs and pancreas are affected most severely.
PLAIN FILM 

•  Bronchiectasis (cylindrical at first).
•  Bronchial wall thickening.
•  Hyperinflation (due to air-trapping).
•  Any part of the lungs may be affected, but particularly central zones, upper lobes and apical lower lobes.
•  Look for mucous impaction with atelectasis.
•  Spontaneous pneumothorax.
•  Pulmonary artery enlargement.

HRCT
•  Most sensitive for detecting early change.
Cystic fibrosis. Chest x-ray demonstrating hyperexpanded lungs with upper zone fibrosis, bronchial wall thickening and bronchiectasis affecting the central and upper zones. There is a cavity with a soft tissue focus outlined by a crescent of air (Monad sign; white arrow) in keeping with an aspergilloma.